Upon 48 h TGFβ exposure (Figure 6D), IPF cells exhibited a significantly lower COX-IV and PINK1 expression response and, within TGFβ-treated cells, IPF LRMSC presented significantly lower COX-IV, MFN2, and PINK1 mRNA levels than CON cells. Here, TGFB1 is linked to idiopathic pulmonary fibrosis.