Upon 48 h TGFβ exposure (Figure 6D), IPF cells exhibited a significantly lower COX-IV and PINK1 expression response and, within TGFβ-treated cells, IPF LRMSC presented significantly lower COX-IV, MFN2, and PINK1 mRNA levels than CON cells. This evidence concerns the gene COX4I1 and idiopathic pulmonary fibrosis.