STAC3 and Malignant hyperthermia: In both patients, we found the previously described pathogenic missense variant p.Trp284Ser in homozygosity.<h4>Conclusion</h4>We seek to highlight the need for screening for CMYP13 in patients expressing the typical phenotype of the disease even in the absence of Lumbee Native American ancestry, and to raise awareness to possible complications like malignant hyperthermia in Bailey-Bloch congenital myopathy.