CPT2 and hydrops fetalis: Induced ketolysis in single ventricle physiology—early reports on the use of Sodium-glucose co-transporter-2 inhibitors. The decreased activity of CPT2 in SV patients without HF, and CPT1/CPT2 in SV patients with HF [94], as well as elevated circulating level of carnitine [95] might indicate metabolic perturbations.