Our study confirmed a correlation between the prevalence of Müllerian duct anomalies due to abnormal organogenesis of the uterus and high AMH levels in patients with PCOS, inferring that the association between PCOS and some types of Müllerian duct anomalies, such as unicornuate uterus, could be explained by certain developmental defects that contribute to both PCOS and Müllerian duct anomalies. The gene discussed is AMH; the disease is polycystic ovary syndrome.