Several studies have explored the risk factors for death of SLE-PAH, such as poor cardiac function and exercise capacity; increased mPAP, PVR, BNP/NT-proBNP, and serum uric acid; and high rate of thrombocytopenia, pulmonary vasculitis, and Raynaud’s phenomenon [28–30]. The gene discussed is NPPB; the disease is Thrombocytopenia.