CPT2 and hyperinsulinemic hypoglycemia, familial, 4: The latest findings on proximal tubule redox imbalance and ferroptotic cell death, as well as the regulation of potassium transport in distal tubules, the myopathic form of CPT II deficiency, and ion channel pharmacology present exciting opportunities to find better ways to prevent RIAKI-associated complications such as oxidative stress, hyperkalemia, and metabolic disorders.