Huntington’s disease (HD) is caused by an expansion of CAG repeats in the huntingtin gene (HTT), resulting in mutant HTT carrying an expanded polyglutamine repeat (more than 36Q) in its N-terminal region (Ross and Tabrizi, 2011; Ross et al., 2014; Saudou and Humbert, 2016). This evidence concerns the gene HTT and Huntington disease.