The main tumors related to TFE3 gene fusion include renal cell carcinoma [28, 29], alveolar soft-part sarcoma (ASPS) [30, 31], epithelioid hemangioendothelioma [32], rare ossifying fibromyxoid tumors [33], malignant chondroid syringoma [34], and perivascular epithelioid cell tumors [35]. This evidence concerns the gene TFE3 and neoplasm with perivascular epithelioid cell differentiation.