These histologies include extra-skeletal sarcomas (e.g., chondro-, osteo-, and Ewing sarcomas), Ewing-like sarcomas (e.g., desmoplastic small round cell tumours, CIC-rearranged, and BCOR-rearranged sarcoma), perivascular epithelioid cell tumours (PEComas), clear cell sarcomas, epithelioid sarcomas, angiosarcomas, fibrosarcomas, inflammatory myofibroblastic tumours, and dendritic cell sarcomas, amongst many others [Table 1]. The gene discussed is BCOR; the disease is neoplasm with perivascular epithelioid cell differentiation.