Mutations in the coding DNA for Kv3.3 (KCNC3) result in a unique neurodegenerative disease termed spinocerebellar ataxia type 13 (SCA13) in mammals (including humans), a disease that can be genetically modeled in zebrafish [121–123]. This evidence concerns the gene KCNC3 and spinocerebellar ataxia type 13.