Pseudohypoaldosteronism type II (PHAII), also known as “familial hyperkalemic hypertension (FHHt)” or “Gordon’s syndrome” is a rare Mendelian syndrome characterized by hypertension, hyperkalemia, metabolic acidosis ,and hypercalciuria, which results from the overactivation of thiazide-sensitive sodium chloride cotransport(NCC) [1, 2]. Here, SLC12A3 is linked to metabolic acidosis.