Variants in the ADAMTS2 gene are known to cause dermatosparaxis in humans (Colige et al. 2004; van Damme et al. 2016) as well as in cattle (Colige et al. 1999), sheep (Zhou et al. 2012; Monteagudo et al. 2015; Joller et al. 2017), and dogs (Jaffey et al. 2019). Here, ADAMTS2 is linked to Ehlers-Danlos syndrome, dermatosparaxis type.