We Recommend Making a Specific Diagnosis of Hyperinsulinism Based on Measurements, at a Time of Hypoglycemia, of Plasma Levels of Metabolic Fuels (Beta-Hydroxybutyrate [BOHB] and Free Fatty Acids [FFA]) and Hormones (Insulin, Growth Hormone, Cortisol) and Determination of the Glycemic Response to a Pharmacologic Dose of Glucagon [Grade 1 ⊕⊕⊕○]. This evidence concerns the gene GH1 and hyperinsulinism.