Methylmalonic acidemia (MMA), the most common form of organic acidemia [1], is the result of methylmalonyl COA mutase (MCM) enzyme deficiency or defect in synthesis or transport of its coenzyme, adenosylcobalamin (AdoCbl), or deficiency of methylmalonyl-CoA epimerase enzyme [2, 3]. The gene discussed is MMUT; the disease is inborn organic aciduria.