OXCT1 and hyperinsulinemic hypoglycemia, familial, 4: Metabolic attacks following infection, ketone positivity in blood and urine, and asymptomatic state between attacks all supported succinyl-CoA 3-ketoacid-CoA transferase (SCOT) deficiency, and the compound heterozygosity for the OXCT1 gene complied with the autosomal recessive inheritance (Sasai et al., 2017).