The frequency of mitochondrial DNA polymerase gamma (POLG) mutations, which lead to mitochondrial recessive ataxia syndrome (MIRAS), is also relatively high [24,25,26], Moreover, although Fragile X–Associated Tremor/Ataxia Syndrome (FXTAS) has been reported in Finland [24,27], no epidemiological data are available. Here, POLG is linked to recessive mitochondrial ataxia syndrome.