Other drugs that have shown promise in treating cholestatic liver diseases include pravastatin and fexofenadine (Hayashi and Sugiyama, 2009; Gonzales et al., 2012; Naoi et al., 2014; Gonzales et al., 2015), which have been reported to improve bile excretion and reduce serum bile acid levels in patients with BSEP deficiency. Here, ABCB11 is linked to hyperinsulinemic hypoglycemia, familial, 4.