SMARCA4 and familial rhabdoid tumor: Approximately 35% of patients with an MRT have been diagnosed with germline alterations of a single allele of the hSNF5 gene, and those who carry a germline mutation in either hSNF5 or BRG‐1 tend to be at greater risk to develop the MRT, known as rhabdoid tumor predisposition syndrome (RTPS).80, 81, 82