In contrary, studies on ACC patients (N = 364, respective 36 pediatric individuals, and 94 subjects with ACC) showed the following MMR anomalies: 13.7% had different MMR gene anomalies, respective of 8.57% (non-germline mutations), while 3.2% had LS (MMR germline mutations, N = 3/94 cases) [25,26,35]. This evidence concerns the gene MRC1 and adrenal cortex carcinoma.