In addition to MYO7A (DFNA11, DFNB2, and Usher syndrome type I), OTOF (DFNB9), CDH23 (DFNB12 and Usher syndrome type I), and WHRN (DFNB31) are present within the hair cell or its stereocilia. The gene discussed is OTOF; the disease is Usher syndrome type 1.