Given its prominent role in neutrophil recruitment and activation, FPR1 has been investigated in several inflammatory lung injury models, with FPR1 knock-out ameliorating disease in several models, including acute endotoxin-induced lung injury, DNBS-mediated colitis, as well as models of chronic obstructive pulmonary disease and pulmonary fibrosis [41–44]. Here, FPR1 is linked to pulmonary fibrosis.