As genetic variants associated with MPO-AAV (microscopic polyangiitis, MPA) and PR3-AAV (granulomatosis with polyangiitis, GPA) vasculitis have been extensively discussed in recent reviews [33,119] and summarised in Table 1 and Figure 1, this current article will only briefly touch on selected SNPs in AAV disease aetiology. Here, PRTN3 is linked to vasculitis.