SMARCB1 and schwannomatosis: In comparison, schwannomatosis is caused by mutations of SMARCB1 (SWI/SNF related, matrix associated, actin dependent regulator of chromatin, subfamily B, member 1) (OMIM: 601607) and LZTR1 (Leucine zipper-like transcription regulator 1) (OMIM: 600574) genes on chromosome 22, encoding tumor suppressor proteins [1, 2].