Although the frequency of HLA-A*11:01 allele is lower in Japanese population compared to Chinese and Thai population (Gonzalez-Galarza et al., 2018), HLA-A*11:01 is a high risk factor involved in co-trimoxazole-induced SJS/TEN in Japanese population (Nakamura et al., 2020). The gene discussed is HLA-A; the disease is Schwartz-Jampel syndrome.