Comparing with adult-onset anti-LGI1 encephalitis, which existing a pathognomonic manifestation like FBDS, pediatric anti-LGI1 encephalitis is infrequently reported and shows little similarities in clinical manifestations except typical symptoms associated with limbic encephalitis (Sen et al., 2014; van Sonderen et al., 2016). This evidence concerns the gene LGI1 and encephalitis.