However, we found that CT severity scores [HR (95%CI): 4.02 (1.04–15.60, p = 0.044)], FVC predicted [OR (95%CI): 0.88 (0.81–0.96, p = 0.005)], DLCO predicted [HR (95%CI): 10.60 (0.24–0.84, p = 0.047)], and KL-6 [HR (95%CI): 3.70 (1.46–9.41, p = 0.006)] and SPD [HR (95%CI): 2.58 (1.01–6.59, p = 0.047)] retained their significance in multivariable Cox-regression analysis after controlling for potential confounders (Table 7). This evidence concerns the gene MUC1 and Platelet storage pool disease.