FOXF1 and alveolar capillary dysplasia with misalignment of pulmonary veins: For the follow-up studies, we decided to focus on FOXF1 transcription factor because it’s expression is highly enriched in lung endothelial cells compared to endothelial cells of other organs18,21 and because the FOXF1 loss-of-function gene mutations are linked to ACDMPV, a fatal congenital lung disease with significant fibrotic remodeling13.