The infiltration and proliferation of autoreactive B and T-cells in the exocrine glands of SjS patients is reflected in the main markers of SjS—anti-SSA and anti-SSB antibodies, present in 50–70% and 33–50% of patients, respectively12, and by the presence of focal lymphocytic infiltration in the minor labial SG biopsy13. Here, SSB is linked to Schwartz-Jampel syndrome.