Epstein–Barr (EBV) virus‐associated lymphoma is reported in Artemis syndrome, DGS, RAS guanyl‐releasing protein 1 (RASGRP1) deficiency, CD70 and CD27 deficiencies, XLP, mutations in SH2D1A, XIAP, and ITK, deficiencies of PRKCD, MST1, Coronin‐1A, CTPS1, CD137, MAGT1, or CARMIL2.18, 56, 57. Here, SH2D1A is linked to lymphoma.