The first reported linkage study of FAME (or benign adult familial myoclonus epilepsy) targeted the gene for dentatorubral pallidoluysian atrophy (DRPLA), in which a causative CAG repeat expansion had been discovered, and the GABRB1, GABRB3, and GABRB6 genes.2 The gene discussed is GABRB3; the disease is Dentatorubral pallidoluysian atrophy.