GPAA1 and Friedreich ataxia: Nearly 25% of all FRDA cases do not subscribe to the essential diagnostic criterion for age of onset before 25 years as defined by Harding3 and are referred to as the late-onset FRDA.4 Atypical features in late-onset FRDA are defined by clinically milder disease phenotypes with a much slower disease progression attributed to the smaller size of the expanded repeat on GAA1.5,6