This suspicion of EGIST is further confirmed with positive staining for CD117 and/or DOG-1.[2] Laboratory studies such as blood workup and serum tumor markers are seldom useful in the diagnosis of GISTs or EGISTs unless done to rule out other types of abdominal neoplasms such as neuroendocrine tumors, teratomas, and others.[13] The management of EGIST in our series encompassed both medical and surgical modalities of treatment. Here, KIT is linked to neuroendocrine neoplasm.