<h4>Introduction</h4>Anti-3-hydroxy-3-methylglutaryl-coenzyme A reductase (HMGCR) myopathy is a recently recognized pathology, but appears less common in children and the characteristics of pediatric cases remain unclear.<h4>Case report</h4>We report a pediatric case of anti-HMGCR myopathy accompanied by skin rash. Here, HMGCR is linked to Skin rash.