GATA2 deficiency, due to heterozygous germline mutations in the GATA2 transcription factor, results in a wide spectrum of syndromes, including MonoMAC [174,175,176]; dendritic cell, monocyte, B, and NK lymphoid (DCML) deficiency [177]; familial myelodysplasia/acute myeloid leukemia (f MDS/AML) [178]; Emberger syndrome (entailing deafness, lymphedema, and MDS/AML) [179]; chronic neutropenia [180]; and Warts, Immunodeficiency, Lymphedema, and anogenital Dysplasia (WILD) syndrome [181,182]. Here, GATA2 is linked to monocytopenia with susceptibility to infections.