Other fundus findings reported in CLN3 disease include optic disc pallor, macular atrophy, macular striae, macular oedema, retinal pigment epithelium (RPE) atrophy, RPE granularity, bone spicule formation, epiretinal membrane, arteriolar attenuation, and even a Coats-like reaction [9, 18, 40, 45]. Here, CLN3 is linked to glycogen storage disease VI.