The genetic etiology of LAMM syndrome was first identified in 2007 when Tekin et al. (2007) showed that mutations in the fibroblast growth factor 3 gene (FGF3 – OMIM 164950) co‐segregated with the phenotype in the affected families, and so far, 23 pathogenic or likely pathogenic variants have been reported in ClinVar, HGMD, PubMed, and Web of Science databases. Here, FGF3 is linked to deafness with labyrinthine aplasia, microtia, and microdontia.