SLC26A4 and Incomplete partition of the cochlea type II: Regarding genetic features which can be associated with anatomical abnormalities, it is speculated that a more severe impairment of pendrin (namely if a biallelic SLC26A4 mutation is present) may correlate with a higher inner ear fluid pressure, worse hearing thresholds, and more severe malformations such as wider diameters in EVA and Mondini Malformation, as confirmed by Forli et al. (25).