Therefore, we have compiled from the literature such data for nine neurodegenerative polyglutamine (polyQ) diseases caused by an abnormal expansion of the polyQ tract, namely six spinocerebellar ataxias (SCA) types 1, 2, 6, 7, 17; Machado–Joseph disease (MJD/SCA3); Huntington’s disease (HD); dentatorubral pallidoluysian atrophy (DRPLA); and spinal and bulbar muscular atrophy, X-linked 1 (SMAX1/SBMA), that is now available at EvoPPI3. The gene discussed is ATXN3; the disease is Dentatorubral pallidoluysian atrophy.