Numerous pathologic variants (mutations) in USH1C gene are causative for Usher syndrome type 1 (https://databases.lovd.nl/shared/genes/USH1C), characterized by congenital profound deafness and vestibular dysfunction, combined with visual loss before puberty (Fuster-Garcia et al., 2021; Delmaghani and El-Amraoui, 2022), affecting the sensory epithelia in both the inner ear and the eye. Here, USH1C is linked to Usher syndrome type 1.