In addition to IgA nephropathy characterized by IgA deposition and anti-neutrophil cytoplasmic antibody-associated nephritis without immunoglobulin or complement deposition, C3 nephropathy with positive fluorescent findings of C3 deposition and negative or weak C1q, C4, and immunoglobulin deposition has recently been proposed [28]. Here, C4A is linked to IgA glomerulonephritis.