Recently, in addition to Ewing family tumors, round cell sarcomas with EWSR1 gene fusion, BCOR-rearrangement, and CIC-rearrangement have been recognized as new entities; furthermore FISH and PCR are essential for the differential diagnosis between ES and Ewing family tumors (19). Here, BCOR is linked to Ewing sarcoma/peripheral primitive neuroectodermal tumor.