KID syndrome is a rare, congenital syndrome of the ectoderm that consists of theclinical trial of progressive vascularizing keratitis, SNHL, and skinmanifestations.[12] It hasbeen reported to occur in both an autosomal dominant and recessive manner causedby a heterozygous mutation in the GJB2 gene that encodes forconnexin-26 on chromosome 13q12.[13] KID syndrome was first proposed by Skinner et al[14] and first described via familialoccurrence by Grob et al[15] ina father and daughter. The gene discussed is GJB2; the disease is sensorineural hearing loss disorder.