Neuroepithelial tumors with PATZ1 fusions (NET-PATZ1) are a diverse group of mostly pediatric tumors harboring fusions between nearby chromosome 22q12 region genes, i.e., MN1-PATZ1 or EWSR1-PATZ1 [60] (Table 1). This evidence concerns the gene PATZ1 and neuroepithelial neoplasm.