Hyperornithinemia-Hyperammonemia-Homocitrullinuria (HHH) syndrome or the ornithine translocation deficiency [5] is the rarest autosomal recessive disorder with various genetic mutations on the SLC25A15 (ORNT1 gene), which encodes the mitochondrial ornithine transporter. Here, SLC25A15 is linked to Hyperornithinemia.