OIIA TNK-LPDs are mostly composed of CD8+ T-large granular lymphocytosis/leukaemia (T-LGL), angioimmunoblastic T-cell lymphoma (AITL) with CD4+ T follicular helper (TFH) phenotype, peripheral T-cell lymphoma (PTCL)-not otherwise specified (NOS), or T-LPDs, and rarely of nasal type TNK-cell lymphoma (TNKCL) [5–9]. Here, CD4 is linked to angioimmunoblastic T-cell lymphoma.