Considering that both types of cochlear anomalies are possible, radiographic differences between IP-1 and IP-2 cochlear anomalies in patients with biallelic SLC26A4 pathogenic variants are significant for the surgical stage of cochlear implantation, since the IP-2 anomaly does not have an increased risk of “gushers” and recurrent meningitis, which is typical for IP-1 malformation. Here, SLC26A4 is linked to infectious meningitis.