In total, the majority of patients with biallelic pathogenic variants in the SLC26A4 gene (patient codes 16, 17, and 192) had congenital severe or profound HL (75%), except for a patient with bilateral isolated EVA anomalies (patient code 1091), in whom we registered moderate HL (25%) (Table 2). This evidence concerns the gene SLC26A4 and Hodgkins lymphoma.