The myo-INIs found in OPMD in our study may reflect the PABPN1 accumulation described in the previous report as PABPN1 was colocalized with p62 aggregates in the myonuclei on immunohistochemistry and also because such intra-myonuclear PABPN1 accumulation was absent in other vacuolar myopathies, including OPDM. This evidence concerns the gene SQSTM1 and X-linked myopathy with excessive autophagy.