Gingival papules are oral fibromas that may potentially occur both in MEN1 and other genetic syndromes (such as tuberous sclerosis, Birt-Hogg-Dubé syndrome, and Cowden syndrome), underlying the importance of differential diagnosis between MEN1 and these syndromes when faced with cutaneous and mucosal tumors in addition to other tumors [48,59,99,100]. Here, MEN1 is linked to Birt-Hogg-Dubé syndrome.