8p11 myeloproliferative syndrome (EMS) or stem cell leukemia/lymphoma (SCLL), which is a very rare but aggressive neoplasm with the fibroblast growth factor receptor 1 (FGFR1) rearrangement on chromosome 8p11-12, is recognized as a distinct entity in 2016 World Health Organization (WHO) classification (1). Here, FGFR1 is linked to myeloid neoplasm associated with FGFR1 rearrangement.