REN and Hyperkalemia: This case had c.562C>T and c.772C>T mutations, and the residual enzymatic activity could also rescue the steroidogenesis capacity of fetal Leydig cells because he had developed male external genitalia in the presence of a micropenis, and assessment of RAAS revealed a high renin level and a low Ald level without hyponatremia and hyperkalemia; thus, he was diagnosed with non-classic LCAH.